Carbamoyl phosphate synthetase catalyzes the ATP-dependent synthesis of carbamoyl phosphate from glutamine (EC 6.3.5.5) or ammonia (EC 6.3.4.16) and bicarbonate...
10 KB (921 words) - 06:20, 10 June 2024
Carbamoyl phosphate synthetase I (CPS I) is a ligase enzyme located in the mitochondria involved in the production of urea. Carbamoyl phosphate synthetase...
8 KB (823 words) - 18:15, 20 July 2024
and the synthesis of pyrimidines. Its enzymatic counterpart, carbamoyl phosphate synthetase I (CPS I), interacts with a class of molecules called sirtuins...
4 KB (355 words) - 14:47, 5 January 2024
Carbamoyl phosphate synthetase III (CPS III) is one of the three isoforms of the carbamoyl phosphate synthetase, an enzyme that catalyzes the active production...
14 KB (1,867 words) - 23:23, 3 July 2024
Carbamoyl phosphate synthetase I deficiency (CPS I deficiency) is an autosomal recessive metabolic disorder that causes ammonia to accumulate in the blood...
6 KB (658 words) - 23:00, 26 October 2023
Carbamoyl phosphate synthetase (glutamine-hydrolysing) (EC 6.3.5.5) is an enzyme that catalyzes the reactions that produce carbamoyl phosphate in the cytosol...
6 KB (566 words) - 03:59, 17 June 2024
carbamoyl phosphate synthetase I and requires the use of two ATP molecules. The carbamoyl phosphate then enters the urea cycle. Carbamoyl phosphate is...
21 KB (2,219 words) - 13:28, 25 July 2024
converted into carbamoyl phosphate through the investment of two ATP molecules. This step is facilitated by carbamoyl phosphate synthetase I. The second...
17 KB (1,907 words) - 01:36, 28 August 2023
(OMIM): 237300 - hyperammonemia due to carbamoyl phosphate synthetase I deficiency (carbamoyl phosphate synthetase I) Online Mendelian Inheritance in Man...
16 KB (1,549 words) - 19:30, 6 September 2024
negligible, as is the case with N-acetylglutamate's activity on carbamoyl phosphate synthetase I, for example. A non-regulatory allosteric site is any non-regulatory...
37 KB (4,437 words) - 20:55, 13 August 2024