Galactitol (dulcitol) is a sugar alcohol, the reduction product of galactose. It has a slightly sweet taste. In people with galactokinase deficiency, a...
3 KB (128 words) - 12:09, 20 July 2023
Galactosemia (section Reduction to galactitol)
form, galactitol. Galactitol, however, is not a suitable substrate for the next enzyme in the polyol pathway, polyol dehydrogenase. Thus, galactitol accumulates...
19 KB (1,872 words) - 13:41, 31 October 2024
extremely high levels of galactitol found in the latter. Classic galactosemia patients typically exhibit urinary galactitol levels of only 98 to 800 mmol/mol...
22 KB (2,729 words) - 13:38, 31 October 2024
In enzymology, a galactitol-1-phosphate 5-dehydrogenase (EC 1.1.1.251) is an enzyme that catalyzes the chemical reaction galactitol-1-phosphate + NAD+...
2 KB (150 words) - 14:07, 26 August 2023
In enzymology, a galactitol 2-dehydrogenase (EC 1.1.1.16) is an enzyme that catalyzes the chemical reaction galactitol + NAD+ ⇌ {\displaystyle \rightleftharpoons...
2 KB (130 words) - 14:07, 26 August 2023
The PTS Galactitol (Gat) Family (TC# 4.A.5) is part of the PTS-AG superfamily. The biochemistry of this family is poorly defined. The only well-characterized...
3 KB (331 words) - 18:47, 27 November 2023
Fucitol, also known as L-fucitol, 1-deoxy-L-galactitol, and (2R,3S,4R,5S)-hexane-1,2,3,4,5-pentol, is a sugar alcohol derived from fucoidan which is found...
3 KB (94 words) - 21:10, 16 October 2024
reduction of glucose to sorbitol, as well as the reduction of galactose to galactitol. Too much sorbitol trapped in retinal cells, the cells of the lens, and...
21 KB (2,058 words) - 14:38, 11 September 2024
(5-carbon) Ribitol (5-carbon) Mannitol (6-carbon) Sorbitol (6-carbon) Galactitol (6-carbon) Fucitol (6-carbon) Iditol (6-carbon) Inositol (6-carbon; a...
12 KB (1,197 words) - 23:27, 21 September 2024
recessive metabolic disorder marked by an accumulation of galactose and galactitol secondary to the decreased conversion of galactose to galactose-1-phosphate...
7 KB (725 words) - 15:45, 10 October 2024