Carnitine is a quaternary ammonium compound involved in metabolism in most mammals, plants, and some bacteria. In support of energy metabolism, carnitine...
30 KB (3,278 words) - 20:35, 26 April 2024
Acetylcarnitine (redirect from Acetyl-L-carnitine)
Acetyl-L-carnitine, ALCAR or ALC, is an acetylated form of L-carnitine. It is naturally produced by the human body, and it is available as a dietary supplement...
16 KB (1,833 words) - 03:43, 18 September 2024
Carnitine palmitoyltransferase I (CPT1) also known as carnitine acyltransferase I, CPTI, CAT1, CoA:carnitine acyl transferase (CCAT), or palmitoylCoA transferase...
19 KB (2,464 words) - 00:31, 12 June 2024
Carnitine palmitoyltransferase II deficiency, sometimes shortened to CPT-II or CPT2, is an autosomal recessively inherited genetic metabolic disorder...
26 KB (3,161 words) - 10:19, 29 August 2024
primary carnitine deficiency (SPCD) is an inborn error of fatty acid transport caused by a defect in the transporter responsible for moving carnitine across...
12 KB (1,279 words) - 09:22, 11 April 2023
Carnitine O-acetyltransferase also called carnitine acetyltransferase (CRAT, or CAT) (EC 2.3.1.7) is an enzyme that encoded by the CRAT gene that catalyzes...
14 KB (1,691 words) - 09:21, 3 June 2024
Carnitine-acylcarnitine translocase (CACT) is responsible for passive transport of carnitine and carnitine-fatty acid complexes and across the inner mitochondrial...
2 KB (253 words) - 19:58, 29 August 2024
Carnitine palmitoyltransferase I deficiency is a rare metabolic disorder that prevents the body from converting certain fats called long-chain fatty acids(LCFA)...
7 KB (597 words) - 14:52, 27 October 2023
Carnitine biosynthesis is a method for the endogenous production of L-carnitine, a molecule that is essential for energy metabolism. In humans and many...
14 KB (1,458 words) - 20:09, 4 September 2024
Carnitine-acylcarnitine translocase deficiency is a rare, autosomal recessive metabolic disorder that prevents the body from converting long-chain fatty...
5 KB (398 words) - 13:42, 14 September 2023